Sudden Death by Catecholaminergic Polymorphic Ventricular Tachycardia in Children
Morte Súbita por Taquicardia Ventricular Polimórfica Catecolaminérgica em Criança
Keywords:
Ventricular tachycardia, Cardiac sudden death, TachycardiaAbstract
Catecholaminergic Polymorphic Ventricular Tachycardia (CPVT) is a severe cardiac arrhythmogenic hereditary illness, which affects children and young adults with a structurally healthy heart. Its prevalence is of one case in 10 thousand inhabitants. It is a potentially fatal illness, part of the differential diagnosis of
syncope in children. The present study has the purpose of relating the case of a child that, during the investigation of convulsive syncope, presented sudden death aborted due to CPVT and to describe the diagnosis difficulties of the case, comparing with data from the literature.
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